Compounds
Compounds of formula (I) defined herein exhibit human neutrophil elastase inhibitory properties and are useful for the treatment of disease or conditions in which HNE is implicated.
1. A compound of formula (I):
wherein
A is:
X is:
R 1 is one of the following groups:
n is an integer from 1 to 4;
m is 0 or an integer from 1 to 4;
t is 0 or an integer from 1 to 4;
y is an integer from 1 to 4;
w is an integer from 1 to 4;
z is 0 or 1;
l is 0 or 1;
R 2 is —H or linear or branched —(C 1 -C 4 )alkyl;
R 3 is linear or branched —(C 1 -C 4 )alkyl or R 2 and R 3 may form together a cycloalkyl;
R 4 is -arylene-(C 1 -C 4 )alkylene-NR d R e , -arylene-(C 1 -C 4 )alkylene-N + R a R b R c , -heteroarylene-(C 1 -C 4 )alkylene-NR d R e , -heteroarylene-(C 1 -C 4 )alkylene-N + R a R b R c and heteroaryl, wherein any of such arylene-(C 1 -C 4 )alkylene-NR d R e , -arylene-(C 1 -C 4 )alkylene-N + R a R b R c , -heteroarylene-(C 1 -C 4 )alkylene-NR d R e , -heteroarylene-(C 1 -C 4 )alkylene-N + R a R b R c and heteroaryl may be optionally substituted by one or more —(C 1 -C 4 )alkyl or R 4 is one of the following groups;
R 5 is aryl-(C 1 -C 4 )alkylenoxy-, linear or branched (C 1 -C 4 )alkyl-OC(O)—NH—, —(CH 2 ) t —NR d R e , —(CH 2 ) t —N + R a R b R c , —C(O)—N(R 10 )C 1 -C 4 )alkylene-NR d R e , —C(O)N(R 10 )(C 1 -C 4 )alkylene-N + R a R b R c , —C(O)O(C 1 -C 4 )alkylene-NR d R e , —C(O)O(C 1 -C 4 )alkylene-N + R a R b R c , —(CH 2 ) t NHC(O)—(C 1 -C 4 )alkylene-NR d R e , —(CH 2 )NHC(O)—(C 1 -C 4 )alkylene-N + R a R b R c , or one of the following groups
R 6 is —H, —(C 1 -C 4 )alkyl, aryl-(C 1 -C 4 )alkylene-OCO—, CF 3 C(O)—, aryl-(C 1 -C 4 )alkylene, linear or branched (C 1 -C 4 )alkyl-OC(O)—, —C(O)—(C 1 -C 4 )alkylene-NR d R e , —C(O)—(C 1 -C 4 )alkylene-N + R a R b R c , —C(O)O—(C 1 -C 4 )alkylene-NR d R e , —C(O)O—(C 1 -C 4 )alkylene-N + R a R b R c —C(O)—N(R 10 )(C 1 -C 4 )alkylene-NR d R e , or —C(O)N(R 10 )(C 1 -C 4 )alkylene-N + R a R b R c ;
R a is —(C 1 -C 4 )alkyl;
R b is —(C 1 -C 4 )alkyl;
R c is —(C 1 -C 4 )alkyl, aryl-(C 1 -C 4 )alkylene or heteroaryl-(C 1 -C 4 )alkylene, wherein said heteroaryl-(C 1 -C 4 )alkylene may be optionally substituted by one or more —(C 1 -C 4 )alkyl groups;
R d is H or —(C 1 -C 4 )alkyl;
R e is H or —(C 1 -C 4 )alkyl;
R 7 is —H or —(C 1 -C 4 )alkyl;
R 8 is —H or —(C 1 -C 4 )alkyl;
R 9 is heterocycloalkyl, heterocycloalkyl-(C 1 -C 4 )alkylene-, (C 1 -C 4 )alkylene-NR d R e and (C 1 -C 4 )alkylene-N + R a R b R c ;
R 10 is —H or —(C 1 -C 4 )alkyl; and
* and #, indicate the points of attachment for the radical groups to the rest of the molecule,
wherein any of such heterocycloalkyl, aryl, heteroaryl and aryl-(C 1 -C 4 )alkylene may be optionally substituted by one or more groups independently selected from (C 1 -C 4 )alkyl and OR 7 and wherein the nitrogen atom in the heterocycloalkyl and heteroaryl groups may be quaternized,
or a pharmaceutically acceptable salt thereof.
2. A compound or salt according to claim 1 , wherein
X is
n is 2; m is 2; R 7 is —H; R 5 is aryl-(C 1 -C 4 )alkylenoxy-, linear or branched (C 1 -C 4 )alkyl-OC(O)—NH, C(O)O(C 1 -C 4 )alkylene-N + R a R b R c , —(CH 2 ) t NHC(O)—(C 1 -C 4 )alkylene-NR d R e , —(CH 2 ) t NHC(O)—(C 1 -C 4 )alkylene-N + R a R b R c , or —C(O)N(R 10 )(C 1 -C 4 )alkylene-N + R a R b R c — wherein t is 0 or 1, R a and R b are independently —(C 1 -C 4 )alkyl, R c is —(C 1 -C 4 )alkyl, heteroaryl-(C 1 -C 4 )alkylene or aryl-(C 1 -C 4 )alkylene, R d and R e are independently —(C 1 -C 4 )alkyl, R 10 is —H or —(C 1 -C 4 )alkyl.
3. A compound or salt according to claim 1 , wherein,
X is
n is 2; m is 2; R 7 is —H; R 5 is —(CH 2 ) t —NR d R e , or —(CH 2 ) t —N + R a R b R c , wherein t is 0 or 1, R a and R b are independently —(C 1 -C 4 )alkyl, R c is —(C 1 -C 4 )alkyl, heteroaryl-(C 1 -C 4 )alkylene or aryl-(C 1 -C 4 )alkylene.
4. A compound or salt according to claim 1 , wherein
X is
n is 2; m is 2; R 7 is —H; R 5 is
R a is —(C 1 -C 4 )alkyl; R b is —(C 1 -C 4 )alkyl; R 10 is —H.
5. A compound or salt according to claim 1 , wherein
X is
n is 2; m is 2; R 7 is —H; R 5 is
R a is —(C 1 -C 4 )alkyl; R b is —(C 1 -C 4 )alkyl.
6. A compound or salt according to claim 1 , wherein
X is
n is 2; m is 2; R 7 is —H or —(C 1 -C 4 )alkyl; R 6 is aryl-(C 1 -C 4 )alkylenoxy-, aryl-(C 1 -C 4 )alkylene-OCO—, CF 3 C(O)—, —C(O)—(C 1 -C 4 )alkylene-NR d R e , —C(O)O—(C 1 -C 4 )alkylene-N + R a R b R c , —C(O)N(R 10 )(C 1 -C 4 )alkylene-N + R a R b R c , or —C(O)—(C 1 -C 4 )alkylene-N + R a R b R c wherein R d is —H or —(C 1 -C 4 )alkyl; R e is —H or —(C 1 -C 4 )alkyl, R a is —(C 1 -C 4 )alkyl; R b is —(C 1 -C 4 )alkyl; R c is selected from —(C 1 -C 4 )alkyl; R 10 is —H.
7. A compound or salt according to claim 1 , wherein
X is
n is 2; m is 2; R 7 is —H or —(C 1 -C 4 )alkyl; R a and R b are each independently —(C 1 -C 4 )alkyl.
8. A compound or salt according to claim 1 , wherein
X is
n is 2; m is 2; R 7 is —H; R 5 is —(CH 2 ) t —N + R a R b R c , R a and R b are each independently —(C 1 -C 4 )alkyl, and R c is aryl-(C 1 -C 4 )alkylene.
9. A pharmaceutical composition, comprising a compound or salt according to claim 1 and a pharmaceutically acceptable carrier or excipient.
10. A pharmaceutical composition according to claim 9 which is adapted for oral administration or administration by the pulmonary route.
11. A method of treatment of a disease or condition in which HNE is implicated, comprising administering to a subject in need thereof an effective amount of a compound or salt according to claim 1 .
12. A method according to claim 11 , wherein said disease or condition is chronic obstructive pulmonary disease, bronchiectasis, chronic bronchitis, lung fibrosis, pneumonia, acute respiratory distress syndrome, pulmonary emphysema, smoking-induced emphysema, or cystic fibrosis.
13. A method according to claim 11 , wherein said disease or condition is asthma, rhinitis, psoriasis, atopic dermatitis, non-atopic dermatitis, Crohn's disease, ulcerative colitis, or irritable bowel disease.
14. A method according to claim 11 , wherein said disease or condition is chronic obstructive pulmonary disease.
15. A method according to claim 11 , wherein said disease or condition is bronchiectasis.
16. A method according to claim 11 , wherein said disease or condition is chronic bronchitis.
17. A method according to claim 11 , wherein said disease or condition is lung fibrosis.
18. A method according to claim 11 , wherein said disease or condition is pneumonia.
19. A method according to claim 11 , wherein said disease or condition is acute respiratory distress syndrome.
20. A method according to claim 11 , wherein said disease or condition is asthma.