Compositions and methods for treating facioscapulohumeral dystrophy
View Patent ↗Compositions and methods for treating FSHD and for identifying agents useful for the treatment of FSHD.
1. A method for suppressing DUX4 toxicity in a cell, the method comprising contacting a cell overexpressing DUX4 with an agent that reduces the expression or activity of a hypoxia response pathway protein selected from the group consisting of hypoxia-inducible factor 1-alpha (HIF1A), hypoxia-inducible factor 1-beta (HIF1B), aryl hydrocarbon receptor nuclear translocator (ARNT), CREB binding protein (CREBBP), CBP, and zinc finger CCHC-type containing 14 (ZCCHC14), wherein the agent is Herbimycin A, Herceptin, Iressa, calphostin C, wortmannin, LY294002, PD98059, rapamycin, diphenylene iodonium, mannoheptulose, 4-Chloro-3-(trifluoromethyl)phenyl isocyanate (CAS 327-78-6), Sterigmatocystin, Chetomin, Cryptotanshione, EF-24, FM19G11, and PX 12.